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  • 產(chǎn)品名稱:EHHADH抗原(重組蛋白)

  • 產(chǎn)品型號:1mg
  • 產(chǎn)品廠商:通蔚生物
  • 產(chǎn)品價格:3580
  • 產(chǎn)品庫存:35
  • 產(chǎn)品文檔:
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詳情介紹:
中文名稱: EHHADH抗原(重組蛋白)

英文名稱: EHHADH Antigen (Recombinant Protein)

別     名:  LBP; ECHD; LBFP; PBFE; L-PBE

儲     存:  冷凍(-20℃)

相關類別: 抗原

概     述:

Fusion protein corresponding to a region derived from 283-572 amino acids of human EHHADH

技術規(guī)格

Full name:

enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase

Synonyms:

LBP; ECHD; LBFP; PBFE; L-PBE

Swissprot:

Q08426

Gene Accession:

BC038948

Purity:

>85%, as determined by Coomassie blue stained SDS-PAGE

Expression system:

Escherichia coli

Tags:

His tag C-Terminus, GST tag N-Terminus

Background:

The protein encoded by this gene is a bifunctional enzyme and is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of the encoded protein contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in this gene are a cause of peroxisomal disorders such as Zellweger syndrome. Two transcript variants encoding different isoforms have been found for this gene.





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